Dermatological Manifestations

dc.contributorSistema FMUSP-HC: Faculdade de Medicina da Universidade de São Paulo (FMUSP) e Hospital das Clínicas da FMUSP
dc.contributor.authorCURY-MARTINS, J.
dc.contributor.authorSANCHES, J. A.
dc.date.accessioned2023-12-04T19:36:21Z
dc.date.available2023-12-04T19:36:21Z
dc.date.issued2023
dc.description.abstractCutaneous involvement by amyloidosis is characterized by extracellular deposition of amyloid protein within the skin and appendages and can occur as a skin-limited disorder (localized cutaneous amyloidosis—LCA) or as a manifestation of systemic amyloidosis (SA). LCA can be divided into primary LCA—macular, lichen and nodular amyloidosis; or secondary LCA. The main subtypes of SA with cutaneous involvement include immunoglobulin light chain (AL) amyloidosis, secondary (AA) amyloidosis, dialysis-related amyloidosis, and heredofamilial amyloidosis. Skin involvement is present, for example, in approximately 40% of patients with AL amyloidosis, and might provide an early clue to the existence of an underlying plasma-cell dyscrasia. © The Editor(s) (if applicable) and The Author(s), under exclusive license to Springer Nature Switzerland AG 2023.
dc.identifier.citationCury-Martins, J.; Sanches, J. A.. Dermatological Manifestations. In: . Amyloidosis and Fabry Disease: a Clinical Guide: SPRINGER INTERNATIONAL PUBLISHING, 2023. p.97-105.
dc.identifier.doi10.1007/978-3-031-17759-0_10
dc.identifier.isbn978-303117759-0; 978-303117758-3
dc.identifier.urihttps://observatorio.fm.usp.br/handle/OPI/57184
dc.language.isoeng
dc.publisherSPRINGER INTERNATIONAL PUBLISHING
dc.relation.ispartofAmyloidosis and Fabry Disease: a Clinical Guide
dc.rightsrestrictedAccess
dc.rights.holderCopyright SPRINGER INTERNATIONAL PUBLISHING
dc.subjectLichen amyloidosis
dc.subjectLocalized cutaneous amyloidosis
dc.subjectMacular amyloidosis
dc.subjectNodular amyloidosis
dc.subjectSkin
dc.subjectSystemic amyloidosis with cutaneous involvement
dc.titleDermatological Manifestations
dc.typebookPart
dc.type.categorybook chapter
dc.type.versionpublishedVersion
dspace.entity.typePublication
hcfmusp.citation.scopus0
hcfmusp.contributor.author-fmusphcJADE CURY MARTINS ASFORA LINS
hcfmusp.contributor.author-fmusphcJOSE ANTONIO SANCHES JUNIOR
hcfmusp.description.beginpage97
hcfmusp.description.endpage105
hcfmusp.origemScopus
hcfmusp.origem.scopus2-s2.0-85171014254
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