Duodenal adenoma surveillance in patients with familial adenomatous polyposis
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Tipo de produção
article
Data de publicação
2015
Editora
BAISHIDENG PUBLISHING GROUP INC
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Título da Revista
ISSN da Revista
Título do Volume
Autores
MARTINEZ, Carlos Augusto Real
Autor de Grupo de pesquisa
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Citação
WORLD JOURNAL OF GASTROINTESTINAL ENDOSCOPY, v.7, n.10, p.950-959, 2015
Resumo
Familial adenomatous polyposis (FAP) is a hereditary disorder caused by Adenomatous Polyposis Gene mutations that lead to the development of colorectal polyps with great malignant risk throughout life. Moreover, numerous extracolonic manifestations incorporate different clinical features to produce varied individual phenotypes. Among them, the occurrence of duodenal adenomatous polyps is considered an almost inevitable event, and their incidence rates increase as a patient's age advances. Although the majority of patients exhibit different grades of duodenal adenomatosis as they age, only a small proportion (1%-5%) of patients will ultimately develop duodenal carcinoma. Within this context, the aim of the present study was to review the data regarding the epidemiology, classification, genetic features, endoscopic features, carcinogenesis, surveillance and management of duodenal polyps in patients with FAP.
Palavras-chave
Familial adenomatous polyposis, Adenoma, Duodenum, Surveillance, Endoscopy, Digestive system
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