Cardiovascular Manifestations of Erdheim-Chester's Disease: A Case Series

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Arquivos
art_COSTA_Cardiovascular_Manifestations_of_ErdheimChesters_Disease_A_Case_Series_2018_eng.PDF (397.01 KB)
art_COSTA_Cardiovascular_Manifestations_of_ErdheimChesters_Disease_A_Case_Series_2018_por.PDF (420.41 KB)
Citações na Scopus
6
Tipo de produção
article
Data de publicação
2018
DOI
SciELO
Scopus
Web of Science
PubMed
Título da Revista
ISSN da Revista
Título do Volume
Editora
ARQUIVOS BRASILEIROS CARDIOLOGIA
Autores
Citação
ARQUIVOS BRASILEIROS DE CARDIOLOGIA, v.111, n.6, p.852-855, 2018
Projetos de Pesquisa
Unidades Organizacionais
Fascículo
Resumo
Erdheim-Chester Disease is a rare entity, classified as an inflammatory myeloid neoplasm, with an unknown incidence, occurring preferentially in men after 50 years of age. Classically, it has a multisystemic presentation, with the skeletal system being the most frequently affected (90% of the patients), followed by genitourinary involvement in 60% of cases and central nervous system in the pituitary and diabetes insipidus in 25% of the cases. Cardiovascular manifestations are present in more than half of the patients, with aortic infiltration and atrial pseudotumor being the most common forms.
Palavras-chave
Erdheim-Chester Disease/diagnosis, Erdheim-Chester Disease/drug therapy, Erdheim-Chester Disease/pathology, Biopsy, Prognosis
URI
https://observatorio.fm.usp.br/handle/OPI/29879
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Coleções
Artigos e Materiais de Revistas Científicas - FM/MCP
Artigos e Materiais de Revistas Científicas - FM/MCM
Artigos e Materiais de Revistas Científicas - HC/ICESP
Artigos e Materiais de Revistas Científicas - HC/InCor
Artigos e Materiais de Revistas Científicas - LIM/08
Artigos e Materiais de Revistas Científicas - LIM/31
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