Total surgical correction of Lutembacher syndrome associated with partial anomalous connection of the pulmonary veins and tricuspid regurgitation

Sistema FMUSP-HC: Faculdade de Medicina da Universidade de São Paulo (FMUSP) e Hospital das Clínicas da FMUSPPOMERANTZEFF, Pablo M. A.BICHUETTE, Luciana D.VERONESE, Elinthon T.RODRIGUES, Renan C.SPINA, Guilherme S.JATENE, Fabio B.2021-10-202021-10-202021AMERICAN JOURNAL OF CARDIOVASCULAR DISEASE, v.11, n.4, p.499-503, 20212160-200Xhttps://observatorio.fm.usp.br/handle/OPI/42143Lutembacher syndrome is characterized by the association of mitral stenosis and atrial septal defect (ASD), usually of the ostium secundum type. The association between superior vena cava-type ASD and partial anomalous pulmonary venous connection is unusual and there are few descriptions in the literature. We report this condition in a 24-year-old woman who was admitted to the hospital with a 1-year history of progressive dyspnea and describe the successful surgical repair following mitral commissurotomy and tunneling of the anomalous pulmonary veins to the left atrium, which determines the closure of the ASD and tricuspid repair.engrestrictedAccessLutembacher syndromemitral stenosisatrial septal defectanomalous pulmonary venous connectionTotal surgical correction of Lutembacher syndrome associated with partial anomalous connection of the pulmonary veins and tricuspid regurgitationarticleCopyright E-CENTURY PUBLISHING CORPCardiac & Cardiovascular Systems