Sistema FMUSP-HC: Faculdade de Medicina da Universidade de São Paulo (FMUSP) e Hospital das Clínicas da FMUSPMICHELSON, Sarah J.CIONGOLI, Marina R.ELNER, Victor M.KAHANA, Alon2019-01-172019-01-172018OPHTHALMIC PLASTIC AND RECONSTRUCTIVE SURGERY, v.34, n.6, p.E201-E203, 20180740-9303https://observatorio.fm.usp.br/handle/OPI/30165Microphthalmia is defined by a globe axial length greater than or equal to 2 standard deviations below the age-adjusted mean and can occur as part of a broader syndrome. The presence of a colobomatous cyst with microphthalmia signifies failure of the embryonic neuroectodermal fissure to close appropriately during development of the globe, creating a protuberant globular appendage that inhibits normal growth and development of the eye itself. Cystic reaccumulation of fluid is common after aspiration or surgical removal. Here, the authors describe a case of a young boy with a colobomatous cyst who underwent eyelid-sparing orbital exenteration followed by reconstruction with absorbable gelatin sponge (Gelfoam, Pfizer, Inc.) and the chemotherapeutic agent bleomycin to promote scarring, achieving the equivalent of a biointegrated implant and facilitating satisfactory placement of an ocular prosthesis. A 2-year follow-up MRI revealed adequate volume in the posterior orbit.engrestrictedAccesscongenital microphthalmosmanagementarticleCopyright LIPPINCOTT WILLIAMS & WILKINS10.1097/IOP.0000000000001246OphthalmologySurgery1537-2677