Sistema FMUSP-HC: Faculdade de Medicina da Universidade de São Paulo (FMUSP) e Hospital das Clínicas da FMUSPGIBELLI, Nelson Elias MendesANDRADE, Wagner de CastroVELHOTE, Manoel Carlos PrietoAYOUB, Ali Abdul RahmanSILVA, Marcos Marques daPINHO-APEZZATO, Maria Lucia deTANNURI, Ana Cristina AounBARROS, Fabio deRICARDI, Luis Roberto SchlaichMOREIRA, Daniel de Albuquerque RangelMIYATANI, Helena ThiePEREIRA, Paulo Renato AlencarTANNURI, Uenis2013-10-112013-10-112013PEDIATRIC TRANSPLANTATION, v.17, n.2, p.195-195, 20131397-3142https://observatorio.fm.usp.br/handle/OPI/2650BACKGROUND/PURPOSE: zPost transplant portal vein thrombosis (PVT)can be extremely disastrous, and portal hypertension and other consequences of the long term privation of portal inflow to the graft may be hazardous, especially in the very young children. Since 1998, Rex shunt has been used successfully to treat these patients. In 2007 we started to perform this surgery in patients with idiopathic PVT and late post transplant PVT. We report our experience with this technique in acute post transplant PVT. METHODS: Case report of six patients (age–12–18 months) submitted to cadaveric (1) and living donor (5) liver transplant (LT). All patients had biliary atresia with portal vein hipoplasia and developed acute portal vein thrombosis (PVT) in the first post-operative day. They were submitted to a mesenteric-portal surgical shunt (Rex shunt) with left internal jugular vein autograft (5) and cadaveric iliac vein graft (1) in the first post-operative day. RESULTS: Current follow-up of 12 months. Postoperative Doppler ultrasounds confirmed shunt patency. There were no biliary complications until now. CONCLUSION: The mesenteric-portal shunt (Rex shunt) with left internal jugular vein autograft should be considered in children with acute PVT after liver transplantation. These children usually have small portal veins, and reanastomosis is often unsuccessful. In addition, this technique has the advantage that we do not manipulate the biliary anastomosis and the hepatic hilum, thus avoiding biliary complications. Although this is an initial experience, we conclude that this technique is feasible, with great benefits for these patients and with low risks.engrestrictedAccessREX SHUNT FOR ACUTE PORTAL VEIN THROMBOSIS AFTER PEDIATRIC LIVER TRANSPLANT IN CHILDREN WITH BILIARY ATRESIAconferenceObjectCopyright WILEY-BLACKWELL10.1111/petr.12037PediatricsTransplantation