Diagnosis and treatment of systemic mastocytosis in Brazil: Recommendations of a multidisciplinary expert panel
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Citações na Scopus
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Tipo de produção
article
Data de publicação
2022
Título da Revista
ISSN da Revista
Título do Volume
Editora
ELSEVIER
Autores
PADULLA, Georgia A.
CERQUEIRA, Ana Maria Mosca de
SOUSA, Adriana Martins de
SANDES, Alex Freire
TRAINA, Fabiola
NOGUEIRA, Frederico Lisboa
PEREIRA, Grazielly de Fathima
BOECHAT, jose Laerte
Citação
HEMATOLOGY TRANSFUSION AND CELL THERAPY, v.44, n.4, p.582-594, 2022
Resumo
Introduction: Systemic Mastocytosis comprises a group of neoplastic diseases character-ized by clonal expansion and infiltration of mast cells into several organs. The diagnosis and treatment of this disease may be challenging for non-specialists. Objective: Make suggestions or recommendations in Systemic Mastocytosis based in a panel of Brazil-ian specialists.Method and results: An online expert panel with 18 multidisciplinary specialists was con-vened to propose recommendations on the diagnosis and treatment of Systemic Mastocy-tosis in Brazil. Recommendations were based on discussions of topics and multiple-choice questions and were graded using the Oxford Centre for Evidence-Based Medicine 2011 Lev-els of Evidence Chart. Conclusion: Twenty-two recommendations or suggestions were proposed based on a litera-ture review and graded according to the findings.(c) 2022 Associacao Brasileira de Hematologia, Hemoterapia e Terapia Celular.
Palavras-chave
Mastocytosis, Expert panel, Adults, Children, Diagnosis, Treatment
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Artigos e Materiais de Revistas Científicas - HC/ICHC
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Artigos e Materiais de Revistas Científicas - LIM/31
Artigos e Materiais de Revistas Científicas - LIM/60