Generalized pustular psoriasis (von Zumbusch)
dc.contributor | Sistema FMUSP-HC: Faculdade de Medicina da Universidade de São Paulo (FMUSP) e Hospital das Clínicas da FMUSP | |
dc.contributor.author | ROMITI, Ricardo | |
dc.contributor.author | HIRAYAMA, Andre Luis da Silva | |
dc.contributor.author | ARNONE, Marcelo | |
dc.contributor.author | MAGALHAES, Renata Ferreira | |
dc.date.accessioned | 2022-08-12T17:18:53Z | |
dc.date.available | 2022-08-12T17:18:53Z | |
dc.date.issued | 2022 | |
dc.description.abstract | Generalized pustular psoriasis (von Zumbusch) is a rare and acute eruption characterized by multiple sterile pustules over an erythematous and edematous background, eventually associated with psoriasis vulgaris. Classically, it manifests as a potentially severe systemic picture and demands prompt diagnosis and intervention. The duration of each flare-up and intervals between the pustular episodes is extremely variable. Recently, genetic abnormalities have been identified mainly in the familial and early variants of this disease. The therapeutic arsenal is limited; however, new drugs being evaluated aim to control both pustular flare-ups and disease recurrences. (C) 2021 Sociedade Brasileira de Dermatologia. | eng |
dc.description.index | MEDLINE | eng |
dc.identifier.citation | ANAIS BRASILEIROS DE DERMATOLOGIA, v.97, n.1, p.63-74, 2022 | |
dc.identifier.doi | 10.1016/j.abd.2021.05.011 | |
dc.identifier.eissn | 1806-4841 | |
dc.identifier.issn | 0365-0596 | |
dc.identifier.uri | https://observatorio.fm.usp.br/handle/OPI/48789 | |
dc.language.iso | eng | |
dc.publisher | ELSEVIER SCIENCE INC | eng |
dc.relation.ispartof | Anais Brasileiros de Dermatologia | |
dc.rights | openAccess | eng |
dc.rights.holder | Copyright ELSEVIER SCIENCE INC | eng |
dc.subject | Acrodermatitis | eng |
dc.subject | Psoriasis | eng |
dc.subject | Psoriasis/epidemiology | eng |
dc.subject | Psoriasis/genetics | eng |
dc.subject | Psoriasis/physiopathology | eng |
dc.subject | Psoriasis/therapy | eng |
dc.subject.other | impetigo herpetiformis | eng |
dc.subject.other | childhood | eng |
dc.subject.other | spectrum | eng |
dc.subject.other | agep | eng |
dc.subject.wos | Dermatology | eng |
dc.title | Generalized pustular psoriasis (von Zumbusch) | eng |
dc.type | article | eng |
dc.type.category | review | eng |
dc.type.version | publishedVersion | eng |
dspace.entity.type | Publication | |
hcfmusp.author.external | MAGALHAES, Renata Ferreira:Univ Estadual Campinas, Fac Ciencias Med, Discipline Dermatol, Campinas, SP, Brazil | |
hcfmusp.citation.scopus | 15 | |
hcfmusp.contributor.author-fmusphc | RICARDO ROMITI | |
hcfmusp.contributor.author-fmusphc | ANDRE LUIS DA SILVA HIRAYAMA | |
hcfmusp.contributor.author-fmusphc | MARCELO ARNONE | |
hcfmusp.description.beginpage | 63 | |
hcfmusp.description.endpage | 74 | |
hcfmusp.description.issue | 1 | |
hcfmusp.description.volume | 97 | |
hcfmusp.origem | WOS | |
hcfmusp.origem.pubmed | 34838431 | |
hcfmusp.origem.scielo | SCIELO:S0365-05962022000100063 | |
hcfmusp.origem.scopus | 2-s2.0-85119917257 | |
hcfmusp.origem.wos | WOS:000748717000010 | |
hcfmusp.publisher.city | NEW YORK | eng |
hcfmusp.publisher.country | USA | eng |
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hcfmusp.scopus.lastupdate | 2024-06-09 | |
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relation.isAuthorOfPublication.latestForDiscovery | 830df912-b6d8-4dec-96d9-77c7eb49d3ee |
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