Generalized pustular psoriasis (von Zumbusch)
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Citações na Scopus
14
Tipo de produção
article
Data de publicação
2022
Título da Revista
ISSN da Revista
Título do Volume
Editora
ELSEVIER SCIENCE INC
Autores
Citação
ANAIS BRASILEIROS DE DERMATOLOGIA, v.97, n.1, p.63-74, 2022
Resumo
Generalized pustular psoriasis (von Zumbusch) is a rare and acute eruption characterized by multiple sterile pustules over an erythematous and edematous background, eventually associated with psoriasis vulgaris. Classically, it manifests as a potentially severe systemic picture and demands prompt diagnosis and intervention. The duration of each flare-up and intervals between the pustular episodes is extremely variable. Recently, genetic abnormalities have been identified mainly in the familial and early variants of this disease. The therapeutic arsenal is limited; however, new drugs being evaluated aim to control both pustular flare-ups and disease recurrences. (C) 2021 Sociedade Brasileira de Dermatologia.
Palavras-chave
Acrodermatitis, Psoriasis, Psoriasis/epidemiology, Psoriasis/genetics, Psoriasis/physiopathology, Psoriasis/therapy
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