Rheumatic Heart Disease: Pathogenesis and Vaccine
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Citações na Scopus
9
Tipo de produção
article
Data de publicação
2018
Título da Revista
ISSN da Revista
Título do Volume
Editora
BENTHAM SCIENCE PUBL LTD
Citação
CURRENT PROTEIN & PEPTIDE SCIENCE, v.19, n.9, p.900-908, 2018
Resumo
Rheumatic fever (RF) and rheumatic heart disease (RHD) follow untreated S. pyogenes throat infections in children who present susceptible genes that favor the development of autoimmune reactions. In this review, we focus on the genes that confer susceptibility and on the autoimmune reactions that occur due to molecular mimicry between human-tissue proteins and streptococcal M protein. Polyarthritis is the initial manifestation, which can evolve to carditis and severe valve damage; these culminate in rheumatic heart disease (RHD) or Sydenham's chorea, which affects the central nervous system. A perspective on vaccine development to prevent the disease is also discussed.
Palavras-chave
Rheumatic fever, rheumatic heart disease, M protein, genes, cytokines, T and B lymphocytes, heart-tissue proteins, anti-S. pyogenes vaccine
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